Esferocitosis hereditaria. Carolina Cózar Trastorno hemolítico familiar caracterizado por: anemia ictericia intermitente esplenomegalia. Esferocitosis Hereditaria Anemia Esferocitosis Hereditaria 1) Defecto de la membrana del eritrocito. 2) Retención selectiva por el bazo normal. De esta forma es posible el rastreo de la esferocitosis hereditaria y de la Las manifestaciones clínicas como ictericia, esplenomegalia, anemia, aplasia y y sobrecarga de hierro sugiere daño pancréatico por la acumulación, tal como se.
|Published (Last):||24 September 2009|
|PDF File Size:||11.8 Mb|
|ePub File Size:||20.36 Mb|
|Price:||Free* [*Free Regsitration Required]|
Int J Pediatr Hematol Oncol ; 2: Abstract Hematological automates using double beam laser diffraction by artificially spherized red blood cells determine both volume and hemoglobin concentration of a very large number of cells, even indicating percentages of aberrant elements. King on behalf of the General Haematology Task Force of the British Committee for Standards in Haematology Guidelines for the diagnosis and management of hereditary spherocytosis.
De esta forma es posible el rastreo de la esferocitosis hereditaria y de la esferocitosis secundaria. Oxygen affinity and compensated hemolysis in hereditary spherocytosis. Thrombo-embolic disease after splenectomy for hereditary stomatocytosis. This explains the discrepancy between these values. Monitoring of blood glucose and ferritin is recommended.
Laparoscopic partial vs total splenectomy in children with hereditary spherocytosis. Postoperative pulmonary embolism in a young female accompanying with Factor V Leiden mutation and hereditary sypherocytosis.
Esferocitosis hereditaria by Jazmin Cózar Madero on Prezi
Guidelines for the diagnosis and management of hereditary spherocytosis update. The high association of HS with both diabetes and iron overload suggest damage of the endocrine pancreas by the latter, as it is also seen in genetic hemochromatosis.
Patient and physician should be informed of the presence of HS to avoid misinterpretation of concurrent pathological symptoms. Aires, Argentina; 16 2: Hereditary Spherocytosis in Neonates with Hyperbilirubinemia. Am J Hematol ;57 1: Br J Haematol ;93 2: J Lab Clin Med. Hereditary spherocytosis, thrombocytosis, and chronic pulmonary emboli: Splenectomy for hereditary spherocytosis: The Italian survey on hereditary spherocytosis. The identity of hyperchromic RBC and spherocytes as well as their normal percentage have been previously established.
Este hecho explica la discrepancia entre estos valores. Blood Cells Mol Dis ; Clinical symptoms such as jaundice, splenomegaly, anemia, aplasia and biliary calculi prompting a diagnosis of HS are in reality rare.
HS being a hemolytic defect, frequently increased iron overload was not unexpected. Polish Academjy of Sciences? Servicio de ayuda de la revista.
There was a problem providing the content you requested
Thus it becomes possible to screen for both hereditary and secondary spherocytosis. Journal of Medical Cases. Erythroid membrane protein defects in hereditary spherocytosis. Long-term evaluation of the beneficial effect of subtotal splenectomy for management of hereditary spherocytosis.
Se recomienda el monitoreo de glucemia y ferritina. Bienvenido a siicsalud Contacto Inquietudes. A study of 62 Spanish cases. Clinico-hematological profile of hereditary spherocytosis: Applying criteria such as permanence of an increased percentage of spherocytes, family history, biochemical symptoms of esferocitosus and clinical data, we claim a prevalence of generally asymptomatic hereditary spherocytosis HS of 1: Referencias -Mayelin Herrera Garcia. J Thromb Thrombolysis ;17 3: Revista Cubana Hematol Inmunol Hemoter ;18 1: